Abstract: Moyamoya disease is an unusual form of chronic, occlusive cerebrovascular diseasecharacterized by bilateral stenosis or occlusion at the terminal portion of the internal carotid artery(ICA) and an abnormal vascular network (the so-called Moyamoya vessels) at the base of the brain.Revascularization surgery for Moyamoya patients is believed to prevent cerebral ischemic attacksby improving cerebral blood flow; however the optimal treatment regimen for hemorrhagic typeMoyamoya disease has yet to be clearly established. Surgical treatment of the hemorrhagic typeremains controversial. In this review, we summarized the clinical features and the current status ofthe treatment for hemorrhagic type Moyamoya disease.

Key words: Moyamoya disease; Cerebral hemorrhage; Signs andsymptoms; Therapy

摘要： 烟雾病是一种慢性闭塞性脑血管病，表现为双侧颈内动脉末端的进行性狭窄和闭塞，伴随脑底异常血管网生成。脑血管重建术通过改善颅内供血，对治疗缺血型烟雾病有效。而对于出血型烟雾病的治疗，目前仍未找到确实有效的治疗方法，外科手术治疗仍存在争议。本文总结概括了出血型烟雾病的临床特点和治疗现状。

关键词: 脑底异常血管网病; 脑出血; 症状和体征; 治疗